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[单项选择]女童,7岁,皮肤毛发发白,诊断为白化病,患者缺乏的酶是
A. 酪氨酸酶
B. 多巴脱羧酶
C. 酪氨酸羟化酶
D. 酪氨酸转氨酶
E. 苯丙氨酸转氨酶

热门试题:

[判断题]企业应按照《中国石化安全风险评估指导意见》开展风险评估工作,形成基层单位、二级单位和企业级安全风险清单,明确企业管控的重大安全风险,并推荐油田公司重大安全风险。
A.正确
B.错误
[判断题]某纳税良好的企业想申请一笔金信税E贷最高可以申请100万元。
A.正确
B.错误
[单项选择]But let no one think that pleasure is immoral. Pleasure in itself is a great good, all pleasure, but its consequences may be such (31) the sensible person eschews, certain varieties of (32) . Nor need pleasure be gross and sensual. They are wise in their generation (33) have discovered that intellectual pleasure is the most satisfying and the most enduring. It is well to (34) the habit of reading. There are (35) sports in which you can engage to your own satisfaction after you have passed the prime of life; there are no games except patience, chess problems and crossword puzzles that you can play without someone to play them with you. Reading suffers (36) no such disadvantages; there is no occupation--except perhaps needle-work, but that leaves the restless spirit (37) liberty-- which you can more easily (38) up at any moment, for any period, and more easily put (39) when other calls press upon you; there i
A. who
B. which
C. that
D. whom
[单选题]P2 脉冲称为( )
A.(模式)询问脉冲
B.控制脉冲(或旁瓣抑制脉冲)
C.框架脉冲
D.同步脉冲
[单项选择]Fearful of losing her job for good, this lady decided to talk to the manager directly.( )
A. for benefits
B. by luck
C. for ever
D. at hand.
[判断题]特殊工种作业人员应持有职业资格证;
A.正确
B.错误
[多项选择]排污泵轴承发热的处理方法是()。
A. 调整配合
B. 更换轴承
C. 适量添加或更换润滑油
D. 更换泵轴或改用推力轴承
[单项选择]关于动脉粥样硬化的发病机制,目前被较多学者支持的是:()
A. 脂质浸润学说
B. 血小板聚集和血栓形成学说
C. 单克隆学说
D. 损伤反应学说
E. 以上都不正确
[多选题] 根据《治安管理处罚法》的规定,举办文化、体育等大型群众性活动,违反有关规定,有发生安全事故危险的情况,公安机关可以采取的措施有( )。

A.强行驱散

B.责令停止活动

C.取缔

D.立即疏散
[多选题]下列关于建筑施工现场职工宿舍的叙述,正确的是(  )。
A.宿舍必须设置可开启式外窗
B.宿舍内应保证有必要的生活空间,室内通道宽度不得小于0.9m
C.宿舍内床铺不得超过2层
D.严禁使用通铺
E.宿舍临时用电宜使用安全电压,采用强电照明的宜使用限流器
[单选题]电化区段计算机联锁设备的接地电阻≤( )。
A.1Ω
B.2Ω
C.3Ω
D.4Ω
[判断题]中国民用航空局公安局负责制定背景调查工作的政策、标准。
A.正确
B.错误
[简答题]电磁透镜的像差有哪几种?
[判断题]不准随意对设备拆卸分解、切割焊接。( )
A.正确
B.错误
[单项选择]对营卫二气的错误描述是()
A. 清者为营,浊者为卫
B. 行血气而营阴阳
C. 营在脉中,卫在脉外
D. 营卫二气五十度而复大会
E. 营气者,泌其津液,注之于脉
[判断题]“税融贷”业务中,客户在原最高额综合授信额度基础上增加“税融贷”授信额度的,最高额综合授信额度的审批由各一级支行终审。
A.正确
B.错误
[单选题]凡在离地面(坠落高度基准面)( )米及以上的地点进行的工作,都应视作高处作业。
A.1
B.1.5
C.2
D.3
[单选题]往复压缩机的最大压缩比是容积系数()时的压缩比
A.最大
B.最小
C.为零
D.为90%
[多项选择]刑法第三百三十八条、第三百三十九条规定的行为,具有下列情形之一的,应当认定为“后果特别严重”:()
A. 致使基本农田、防护林地、特种用途林地十五亩以上,其他农用地三十亩以上,其他土地六十亩以上基本功能丧失或者遭受永久性破坏的
B. 致使森林或者其他林木死亡一百五十立方米以上,或者幼树死亡七千五百株以上的
C. 致使疏散、转移群众一万五千人以上的
D. 致使一人以上死亡或者重度残疾的
[单项选择]

Mart’s story in China began many thousands of years ago. Remains of an early form of man discovered in China, known as Peking Man, indicate that Stone Age men lived in the area as long as 500,000 years ago. During the centuries that followed, their descendants laid the foundations of civilization in Chin

  • a.
    Throughout its history, China has been a rich source of inventions. Silk, the compass, tea and porcelain originated there. In addition, they are responsible for the invention of paper and printing. The Chinese had used ink as early as 1 200B.C. , an excellent type which they made from lampblack and which is known in English as India ink or China ink. By the end of the first centuryA.D. , the Chinese had invented paper.
    The Chinese also invented printing. Early Chinese printing is called block printing. The printer carved raised characters on a block of wood, wet the surface of the characters with ink, and pressed sheets of pap
    A. New Stone Man
    B. Silk Man
    C. Peking Man
    D. India Man
[单选题]不属于WAN的网络类型是()。
A.综合业务数字网:ISDN
B.以太网
C.X.25共用分组交换网
D.异步传输模式:ATM
[判断题]CTC应具备分散自律控制和非常站控两种模式。(高铁技规第85条)
A.正确
B.错误
[单项选择]1968年世界医学会规定了医生确定死亡的道德责任和器官移植的道德原则是()
A. 《赫尔辛基宣言》
B. 《日内瓦宣言》
C. 《东京宣言》
D. 《夏威夷宣言》
E. 《悉尼宣言》
[多项选择]在( )情况下,委托代理终止。
A. 被代理人取得或恢复民事行为能力
B. 指定代理的人民法院或者指定单位取消指定
C. 代理期间届满或者代理事务完成
D. 代理人丧失民事行为能力
E. 被代理人取消委托或者代理人辞去委托
[单项选择]

Mary was very fond of television, so when she met a young man (36) worked for a television company, she was very (37) and asked him a lot of questions. She discovered that he had also worked for a film company, so she asked him (38) there was any difference (39) film work and television. " (40) ," answered the young man, "there is one very big (41) . If someone makes a (42) while a film is being made, it is, of course, (43) to stop and do the scene again. In fact, one can do it over and over again a lot of (44) . Mistakes (45) time, money and films, but the audience (观众) who see the film (46) it is finished don’t know that anything went wrong. In a live (实况播送的) television show, (47) the audience can see any mistakes that are made. I can tell you a story about that. (48) ,a live television show (49) and one of the actors was supposed (50) . He fell to theA. eat
B. pull
C. clean
D. apologize to

[判断题]爆炸物质在爆炸过程中都是由化学爆炸引起的。( )
A.正确
B.错误
[单项选择]甲在乙拥有使用权的土地上设立地役权并办理了等级,乙将自己的土地使用权让给丙,()。
A. 甲的地役权因办理等级而设立
B. 乙转让土地使用权应经甲同意
C. 土地所有权人设立地役权不必经乙同意
D. 甲的地役权对丙具有约束力
[简答题]《供用电营业规则》中规定用户申请新装或增加用电时,应向供电企业提供什么资料?
[填空题]在线路允许速度120km/h<υmax≤160km/h正线混凝土枕线路上,线路轨道静态几何尺寸容许偏差管理值中,水平的作业验收标准为( )mm。
[单项选择]将临时性建筑、防水要求很低的建筑,如工棚、随工艺要求而不断改变布局的车间、临时性库房、车棚等划分为______级。
A. Ⅰ
B. Ⅱ
C. Ⅲ
D. Ⅳ
[填空题]录井施工设计修改后必须()、()。
[多项选择]男性,25岁,饮酒后左上腹疼痛伴呕吐9h,呈持续性剧痛,向左腰背部放射,呕吐后疼痛无缓解。查体:血压80/50mmHg,脉搏124/分钟,呼吸24/分钟,体温37.9℃。急性痛苦容,烦躁。左上腹压痛明显,墨菲征阴性,腹水征阳性,肠鸣音弱。血淀粉酶明显升高。患者临床诊断为重症胰腺炎,其病理特点为()
A. 钙皂斑
B. 胰腺腺泡细胞及脂肪坏死、血管出血
C. 坏死灶外周大量炎性细胞浸润
D. 脓肿、假性囊肿或瘘管形成
E. 静脉炎、淋巴管炎和血栓形成
F. 胰腺干酪样坏死
G. 胰腺间质充血、坏死和炎症细胞浸润,无或少量腺泡坏死,血管变化不明确
[判断题]从业人员在300人以上不足1000人的,应当设置专门的安全生产管理机构,并按不低于从业人员5‰但最低不少于3名的比例配备专职安全生产管理人员,其中至少应当有2名注册安全工程师。( )
A.正确
B.错误
[名词解释]OSI
[填空题]最高管理者应确定质量目标及测量要求,并必须包含在(),用于()。
[单选题]DAB型集成装置是通过( )查看空气制动的缓解、制动位。
A.三角形行程指示器在行程标志牌上的相应位置
B.外套筒上的黄色行程指示器在伸缩杆上相应颜色的行程标志环带内
C.鞲鞴推杆伸缩情况
D.闸瓦是否紧贴车轮踏面

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